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Scot Leary
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Mutations in COX15 produce a defect in the mitochondrial heme biosynthetic pathway, causing early-onset fatal hypertrophic cardiomyopathy
H Antonicka, A Mattman, CG Carlson, DM Glerum, KC Hoffbuhr, SC Leary, ...
The American Journal of Human Genetics 72 (1), 101-114, 2003
3762003
Mutations in COX10 result in a defect in mitochondrial heme A biosynthesis and account for multiple, early-onset clinical phenotypes associated with isolated COX deficiency
H Antonicka, SC Leary, GH Guercin, JN Agar, R Horvath, NG Kennaway, ...
Human molecular genetics 12 (20), 2693-2702, 2003
3042003
A Targetable Fluorescent Sensor Reveals That Copper-Deficient SCO1 and SCO2 Patient Cells Prioritize Mitochondrial Copper Homeostasis
SC Dodani, SC Leary, PA Cobine, DR Winge, CJ Chang
Journal of the American Chemical Society 133 (22), 8606-8616, 2011
2922011
Human SCO1 and SCO2 have independent, cooperative functions in copper delivery to cytochrome c oxidase
SC Leary, BA Kaufman, G Pellecchia, GH Guercin, A Mattman, M Jaksch, ...
Human molecular genetics 13 (17), 1839-1848, 2004
2802004
The human cytochrome c oxidase assembly factors SCO1 and SCO2 have regulatory roles in the maintenance of cellular copper homeostasis
SC Leary, PA Cobine, BA Kaufman, GH Guercin, A Mattman, J Palaty, ...
Cell metabolism 5 (1), 9-20, 2007
2662007
p53 improves aerobic exercise capacity and augments skeletal muscle mitochondrial DNA content
JY Park, P Wang, T Matsumoto, HJ Sung, W Ma, JW Choi, SA Anderson, ...
Circulation research 105 (7), 705-712, 2009
2172009
Human Sco1 and Sco2 function as copper-binding proteins
YC Horng, SC Leary, PA Cobine, FBJ Young, GN George, EA Shoubridge, ...
Journal of Biological Chemistry 280 (40), 34113-34122, 2005
1922005
Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1
SC Leary, F Sasarman, T Nishimura, EA Shoubridge
Human molecular genetics 18 (12), 2230-2240, 2009
1912009
Regulation of muscle mitochondrial design
CD Moyes, BJ Battersby, SC Leary
Journal of Experimental Biology 201 (3), 299-307, 1998
1541998
“Pulling the plug” on cellular copper: the role of mitochondria in copper export
SC Leary, DR Winge, PA Cobine
Biochimica et Biophysica Acta (BBA)-Molecular Cell Research 1793 (1), 146-153, 2009
1462009
The mitochondrion: a central architect of copper homeostasis
ZN Baker, PA Cobine, SC Leary
Metallomics 9 (11), 1501-1512, 2017
1332017
Interactions between bioenergetics and mitochondrial biogenesis
SC Leary, BJ Battersby, RG Hansford, CD Moyes
Biochimica et biophysica acta (BBA)-bioenergetics 1365 (3), 522-530, 1998
1311998
Getting out what you put in: Copper in mitochondria and its impacts on human disease
PA Cobine, SA Moore, SC Leary
Biochimica Et Biophysica Acta (BBA)-Molecular Cell Research 1868 (1), 118867, 2021
1302021
The mammalian phosphate carrier SLC25A3 is a mitochondrial copper transporter required for cytochrome c oxidase biogenesis
A Boulet, KE Vest, MK Maynard, MG Gammon, AC Russell, AT Mathews, ...
Journal of Biological Chemistry 293 (6), 1887-1896, 2018
1172018
Copper import into the mitochondrial matrix in Saccharomyces cerevisiae is mediated by Pic2, a mitochondrial carrier family protein
KE Vest, SC Leary, DR Winge, PA Cobine
Journal of Biological Chemistry 288 (33), 23884-23892, 2013
1172013
Fiber-type differences in muscle mitochondrial profiles
SC Leary, CN Lyons, AG Rosenberger, JS Ballantyne, J Stillman, ...
American Journal of Physiology-Regulatory, Integrative and Comparative …, 2003
1132003
Chronic treatment with azide in situ leads to an irreversible loss of cytochrome c oxidase activity via holoenzyme dissociation
SC Leary, BC Hill, CN Lyons, CG Carlson, D Michaud, CS Kraft, K Ko, ...
Journal of Biological Chemistry 277 (13), 11321-11328, 2002
1062002
Human COX20 cooperates with SCO1 and SCO2 to mature COX2 and promote the assembly of cytochrome c oxidase
M Bourens, A Boulet, SC Leary, A Barrientos
Human molecular genetics 23 (11), 2901-2913, 2014
992014
Redox regulation of SCO protein function: controlling copper at a mitochondrial crossroad
SC Leary
Antioxidants & redox signaling 13 (9), 1403-1416, 2010
942010
Elesclomol restores mitochondrial function in genetic models of copper deficiency
S Soma, AJ Latimer, H Chun, AC Vicary, SA Timbalia, A Boulet, JJ Rahn, ...
Proceedings of the National Academy of Sciences 115 (32), 8161-8166, 2018
852018
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