Scot Leary
Title
Cited by
Cited by
Year
Mutations in COX15 produce a defect in the mitochondrial heme biosynthetic pathway, causing early-onset fatal hypertrophic cardiomyopathy
H Antonicka, A Mattman, CG Carlson, DM Glerum, KC Hoffbuhr, SC Leary, ...
The American Journal of Human Genetics 72 (1), 101-114, 2003
3162003
A Targetable Fluorescent Sensor Reveals That Copper-Deficient SCO1 and SCO2 Patient Cells Prioritize Mitochondrial Copper Homeostasis
SC Dodani, SC Leary, PA Cobine, DR Winge, CJ Chang
Journal of the American Chemical Society 133 (22), 8606-8616, 2011
2352011
Human SCO1 and SCO2 have independent, cooperative functions in copper delivery to cytochrome c oxidase
SC Leary, BA Kaufman, G Pellecchia, GH Guercin, A Mattman, M Jaksch, ...
Human molecular genetics 13 (17), 1839-1848, 2004
2342004
Mutations in COX10 result in a defect in mitochondrial heme A biosynthesis and account for multiple, early-onset clinical phenotypes associated with isolated COX deficiency
H Antonicka, SC Leary, GH Guercin, JN Agar, R Horvath, NG Kennaway, ...
Human molecular genetics 12 (20), 2693-2702, 2003
2332003
The human cytochrome c oxidase assembly factors SCO1 and SCO2 have regulatory roles in the maintenance of cellular copper homeostasis
SC Leary, PA Cobine, BA Kaufman, GH Guercin, A Mattman, J Palaty, ...
Cell metabolism 5 (1), 9-20, 2007
2112007
p53 improves aerobic exercise capacity and augments skeletal muscle mitochondrial DNA content
JY Park, P Wang, T Matsumoto, HJ Sung, W Ma, JW Choi, SA Anderson, ...
Circulation research 105 (7), 705-712, 2009
1782009
Human Sco1 and Sco2 function as copper-binding proteins
YC Horng, SC Leary, PA Cobine, FBJ Young, GN George, EA Shoubridge, ...
Journal of Biological Chemistry 280 (40), 34113-34122, 2005
1642005
Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1
SC Leary, F Sasarman, T Nishimura, EA Shoubridge
Human molecular genetics 18 (12), 2230-2240, 2009
1492009
Regulation of muscle mitochondrial design.
CD Moyes, BJ Battersby, SC Leary
Journal of Experimental Biology 201 (3), 299-307, 1998
1341998
“Pulling the plug” on cellular copper: the role of mitochondria in copper export
SC Leary, DR Winge, PA Cobine
Biochimica et Biophysica Acta (BBA)-Molecular Cell Research 1793 (1), 146-153, 2009
1212009
Interactions between bioenergetics and mitochondrial biogenesis
SC Leary, BJ Battersby, RG Hansford, CD Moyes
Biochimica et biophysica acta (BBA)-bioenergetics 1365 (3), 522-530, 1998
1061998
Fiber-type differences in muscle mitochondrial profiles
SC Leary, CN Lyons, AG Rosenberger, JS Ballantyne, J Stillman, ...
American Journal of Physiology-Regulatory, Integrative and Comparative …, 2003
942003
Redox regulation of SCO protein function: controlling copper at a mitochondrial crossroad
SC Leary
Antioxidants & redox signaling 13 (9), 1403-1416, 2010
832010
Chronic treatment with azide in situ leads to an irreversible loss of cytochrome c oxidase activity via holoenzyme dissociation
SC Leary, BC Hill, CN Lyons, CG Carlson, D Michaud, CS Kraft, K Ko, ...
Journal of Biological Chemistry 277 (13), 11321-11328, 2002
832002
Copper import into the mitochondrial matrix in Saccharomyces cerevisiae is mediated by Pic2, a mitochondrial carrier family protein
KE Vest, SC Leary, DR Winge, PA Cobine
Journal of Biological Chemistry 288 (33), 23884-23892, 2013
712013
Human COX20 cooperates with SCO1 and SCO2 to mature COX2 and promote the assembly of cytochrome c oxidase
M Bourens, A Boulet, SC Leary, A Barrientos
Human molecular genetics 23 (11), 2901-2913, 2014
602014
Allometric scaling of RNA, DNA, and enzyme levels: an intraspecific study
GP Burness, SC Leary, PW Hochachka, CD Moyes
American Journal of Physiology-Regulatory, Integrative and Comparative …, 1999
561999
Oxidative phosphorylation: synthesis of mitochondrially encoded proteins and assembly of individual structural subunits into functional holoenzyme complexes
SC Leary, F Sasarman
Mitochondrial DNA, 143-162, 2009
552009
Cooperation between COA6 and SCO2 in COX2 maturation during cytochrome c oxidase assembly links two mitochondrial cardiomyopathies
D Pacheu-Grau, B Bareth, J Dudek, L Juris, FN Vögtle, M Wissel, ...
Cell metabolism 21 (6), 823-833, 2015
472015
Direct Effects of 3, 5, 3′-Triiodothyronine and 3, 5-Diiodothyronine on Mitochondrial Metabolism in the GoldfishCarassius auratus
SC Leary, KN Barton, JS Ballantyne
General and comparative endocrinology 104 (1), 61-66, 1996
461996
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